Please use this identifier to cite or link to this item: https://ahro.austin.org.au/austinjspui/handle/1/27792
Title: Budd-Chiari syndrome in small hepatic veins: A diagnostic and therapeutic challenge in a low resource setting.
Austin Authors: Sultana, Emiko;Hasan, M Tasdik;Mahmood, Hassan Rushekh;Ansar, Adnan;Podder, Vivek;Emrul, Khan;Ali, Md Yusuf
Affiliation: Austin Clinical School of Nursing, La Trobe University
General Surgery, University Hospitals Birmingham NHS Trust, Birmingham, UK
Department of Primary Care and Mental Health, University of Liverpool, Liverpool, UK
Maternal and Child Health Division, International Centre for Diarrheal Diseases Research, Bangladesh, Dhaka, Bangladesh
General Medicine, Tairunnessa Memorial Medical College and Hospital, Gazipur, Bangladesh
General Surgery, Bangabandhu Sheikh Mujib Medical University, Shahbagh, Dhaka, Bangladesh
Internal Medicine, Diabetic Association Medical College, Faridpur, Bangladesh
Issue Date: Aug-2021
Date: 2021-08-27
Publication information: Journal of Family Medicine and Primary Care 2021; 10(8): 3154-3158
Abstract: Budd-Chiari syndrome (BCS) is a rare condition affecting one in a million adults. BCS involves outflow obstruction in the hepatic venous system, which can occur anywhere between the small hepatic veins and the atrio-caval junction and cannot be due to heart, pericardial, or hepatic veno-occlusive disease. We report an exceedingly rare form of BCS with less common initial clinical features in a young poor adult male patient which ignited a diagnostic uncertainty and a therapeutic challenge. The presence of the classical triad of BCS in the absence of major hepatic vein obstruction prompted the medical team to consider that the patient had a rare form of BCS. In this case, the financial condition of the patient and limited resources available restricted our ability to advance into the specific investigations. However, the patient was given symptomatic medical treatment and was followed up monthly. We also provided the patient with a statement that reaffirmed our inability to provide affordable surgical management options and called for an optimized national clinical guideline that could help the physicians deal with the challenges. An uncommon form of BCS in this patient provided a diagnostic challenge and therapeutic uncertainty in the low-resource settings. Primary care physicians should commence evidenced medical management based on clinical suspicion acknowledging the fact that obstruction of small hepatic veins is often not detected on an ultrasound.
URI: https://ahro.austin.org.au/austinjspui/handle/1/27792
DOI: 10.4103/jfmpc.jfmpc_2213_20
Journal: Journal of Family Medicine and Primary Care
PubMed URL: 34660462
ISSN: 2249-4863
Type: Journal Article
Subjects: Budd-Chiari syndrome
low-resource setting
small hepatic vein
Appears in Collections:Journal articles

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