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Title: Myoclonic absence seizures with complex gestural automatisms.
Austin Authors: Myers, Kenneth A;Scheffer, Ingrid E 
Affiliation: Epilepsy Research Centre, Department of Medicine, Austin Health, The University of Melbourne, Heidelberg, Victoria, Australia
Department of Paediatrics, The University of Melbourne, Parkville, Victoria, Australia
The Florey Institute of Neuroscience and Mental Health, Heidelberg, Victoria, Australia
Department of Neurology, Royal Children's Hospital, Parkville, Victoria, Australia
Issue Date: May-2018 2017-12-19
Publication information: European journal of paediatric neurology : EJPN 2018; 22(3): 532-535
Abstract: Epilepsy with myoclonic absences is a rare generalized epilepsy syndrome with distinctive seizures. Two unrelated children had mild developmental impairment and onset of myoclonic-absences at 3 and 8 years. Seizures were characterized by bilateral 3 Hz myoclonic jerks superimposed on tonic abduction of the upper limbs. Events lasted 10-60 s, and complex gestural automatisms were often observed; in one case, a boy undid his seatbelt and attempted to exit a moving vehicle. Post-ictally, both children immediately regained awareness without recollection of their actions. Ictal EEGs showed 3 Hz generalized spike-wave. Complex automatisms have not been described in myoclonic absence seizures. This generalized seizure type can be confused with focal seizures when these ictal behaviours occur.
DOI: 10.1016/j.ejpn.2017.12.003
ORCID: 0000-0002-2311-2174
PubMed URL: 29325826
Type: Journal Article
Subjects: Automatisms
Genetic generalized epilepsy
Myoclonic absence epilepsy
Myoclonic absence seizures
Appears in Collections:Journal articles

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