Austin Health

Title
A rare case of Behçet disease with generalised myositis, cardiomyositis and necrotising fasciitis
Publication Date
2016
Author(s)
Ng, Felix C
Chiong, Fabian Joon Kiong
Buchanan, Russell R C
Burrell, Louise M
Subject
Behcet Syndrome
Myositis
Type of document
Journal Article
DOI
10.1136/bcr-2015-211983
Abstract
Behçet disease (BD) is a rare relapsing, multisystem vasculitis characterised by recurrent oral and genital ulcers, and uveitis. As an autoimmune small vessel vasculitis, BD can involve other organs including the skin, joints, nervous system, kidney and the gastrointestinal tract. This report describes a 40-year-old woman who presented with an uncommon feature of BD, namely myositis, and who went on to develop myocarditis and polymicrobial necrotising fasciitis. To the best of our knowledge, this is the first reported case of an immunocompromised-associated infection occurring in BD without concurrent immunosuppressive therapy.
Link
Citation
BMJ Case Reports 2016; 2016: bcr-2015-211983
Jornal Title
BMJ Case Reports

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