Cystic meningioangiomatosis in neurofibromatosis type 2: an MRI-pathological study.

2009-07-01

Fedi, M

Kalnins, Renate M

Shuey, N

Fitt, Gregory J

Newton, Mark R

Mitchell, L Anne

Journal Article

10.1259/bjr/56536580

We report cerebral cystic meningioangiomatosis in a patient with neurofibromatosis type 2. An 18-year-old woman presented with progressive hemiparesis secondary to a meningioma at the foramen magnum. Her MR examination also demonstrated three small cortical and subcortical cystic lesions. She underwent surgery for the meningioma, but died from brainstem infarction. Post-mortem histopathological examination of the cystic lesions showed enlarged subcortical perivascular spaces with overlying meningioangiomatosis. The unusual features and possible pathogenesis are discussed.

link

The British Journal of Radiology; 82(979): e129-32

The British journal of radiology