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Title: Successful liver transplantation in common variable immune deficiency with reversal of hepatopulmonary syndrome.
Authors: Apostolov, Ross;Sinclair, Marie;Lokan, Julie;Angus, Peter W
Affiliation: Victorian Liver Transplant Unit, Austin Health, Heidelberg, Victoria, Australia
Department of Pathology, Austin Health, Heidelberg, Victoria, Australia
Issue Date: 3-Apr-2019
EDate: 2019-04-03
Citation: BMJ Case Reports 2019; 12(4): e226095
Abstract: Common variable immune deficiency (CVID) is a primary immunodeficiency disorder that is associated with abnormal liver function tests, however advanced liver disease is uncommon. Hepatopulmonary syndrome (HPS) is a rare but debilitating complication of CVID-associated liver disease. We report a case of CVID complicated by HPS that was successfully treated with orthotopic liver transplant, with the patient recovering to normal hepatic function and successfully weaning off domiciliary oxygen post-transplantation.
DOI: 10.1136/bcr-2018-226095
PubMed URL: 30948390
Type: Journal Article
Subjects: immunology
portal hypertension
Appears in Collections:Journal articles

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