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Title: Treatment of idiopathic pulmonary fibrosis in Australia and New Zealand: A position statement from the Thoracic Society of Australia and New Zealand and the Lung Foundation Australia.
Authors: Jo, Helen E;Troy, Lauren K;Keir, Gregory;Chambers, Daniel C;Holland, Anne;Goh, Nicole S L;Wilsher, Margaret;de Boer, Sally;Moodley, Yuben;Grainge, Christopher;Whitford, Helen;Chapman, Sally;Reynolds, Paul N;Glaspole, Ian;Beatson, David;Jones, Leonie;Hopkins, Peter;Corte, Tamera J
Affiliation: Department of Respiratory Medicine, Royal Prince Alfred Hospital, Sydney, NSW, Australia
Faculty of Medicine, University of Sydney, Sydney, NSW, Australia
Department of Respiratory Medicine, Princess Alexandra Hospital, Brisbane, QLD, Australia
Department of Respiratory Medicine, The Prince Charles Hospital, Brisbane, QLD, Australia
Department of Physiotherapy, The Alfred Hospital, Melbourne, VIC, Australia
Department of Respiratory Medicine, Austin Health, Heidelberg, Victoria, Australia..
Department of Respiratory Medicine, Auckland District Health Board, Auckland, New Zealand..
Department of Respiratory Medicine, Fiona Stanley Hospital, Perth, WA, Australia
Department of Respiratory Medicine, John Hunter Hospital, Newcastle, NSW, Australia
Department of Respiratory Medicine, The Alfred Hospital, Melbourne, VIC, Australia
Department of Respiratory Medicine, Royal Adelaide Hospital, Adelaide, SA, Australia
Patient Advocate, Auckland, New Zealand
Issue Date: Oct-2017
EDate: 2017
Citation: Respirology (Carlton, Vic.) 2017; 22(7): 1436-1458
Abstract: Idiopathic pulmonary fibrosis (IPF) is a fibrosing interstitial lung disease (ILD) of unknown aetiology with a median survival of only 2-5 years. It is characterized by progressive dyspnoea and worsening lung function, ultimately resulting in death. Until recently, there were no effective therapies for IPF; however, with the publication of two landmark clinical trials in 2014, the anti-fibrotic therapies, nintedanib and pirfenidone, have gained widespread approval. This position paper aims to highlight the current evidence for the treatment of IPF, with particular application to the Australian and New Zealand population. We also consider areas in which evidence is currently lacking, especially with regard to the broader IPF severity spectrum and treatment of co-morbid conditions. The utility of non-pharmacological therapies including pulmonary rehabilitation, oxygen as well as symptom management thought to be important in the holistic care of IPF patients are also discussed.
DOI: 10.1111/resp.13146
PubMed URL: 28845557
Type: Journal Article
Subjects: nintedanib, pirfenidone
idiopathic pulmonary fibrosis
interstitial lung disease
Appears in Collections:Journal articles

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