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|Title:||Myoclonic absence seizures with complex gestural automatisms.|
|Authors:||Myers, Kenneth A;Scheffer, Ingrid E|
|Affiliation:||Epilepsy Research Centre, Department of Medicine, Austin Health, The University of Melbourne, Heidelberg, Victoria, Australia|
Department of Paediatrics, The University of Melbourne, Parkville, Victoria, Australia
The Florey Institute of Neuroscience and Mental Health, Heidelberg, Victoria, Australia
Department of Neurology, Royal Children's Hospital, Parkville, Victoria, Australia
|Citation:||European journal of paediatric neurology : EJPN 2018; 22(3): 532-535|
|Abstract:||Epilepsy with myoclonic absences is a rare generalized epilepsy syndrome with distinctive seizures. Two unrelated children had mild developmental impairment and onset of myoclonic-absences at 3 and 8 years. Seizures were characterized by bilateral 3 Hz myoclonic jerks superimposed on tonic abduction of the upper limbs. Events lasted 10-60 s, and complex gestural automatisms were often observed; in one case, a boy undid his seatbelt and attempted to exit a moving vehicle. Post-ictally, both children immediately regained awareness without recollection of their actions. Ictal EEGs showed 3 Hz generalized spike-wave. Complex automatisms have not been described in myoclonic absence seizures. This generalized seizure type can be confused with focal seizures when these ictal behaviours occur.|
Genetic generalized epilepsy
Myoclonic absence epilepsy
Myoclonic absence seizures
|Appears in Collections:||Journal articles|
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